ANCA
Occurrence of the ANCA
- Disease Prevalence ANCA positive Antigen specificity
- GPA 24/mio 40% - 98% PR3
- MPA 25/mo 60% - 75% MPO
- eGPA 10/mio 35% - 40% MPO
ANCA-associated small vessel vasculitis without immune complex formation
- Granulomatosis with polyangiitis
- Microscopic polyangiitis
- Eosinophilic granulomatosis with polyangiitis
- Renal limited ANCA vasculitis
ANCA-associated glomerulopathy
Membranous nephropathy Lupus nephritis IgA nephropathy
Small vessel vasculitis with immune complex formation
Goodpasture's disease
Medicines/ Substances
Propylthiouracil Levamisol (an agent for "stretching" cocaine)
inflammatory bowel disease
Colitis ulcerosa Primary biliary cirrhosis
Infections
In the context of bacteremia Subacute endocarditis Tbc Aspergillosis
Non-vasculitic rheumatic diseases, which can feign a non-specific ANCA titer
Systemic lupus erythematosus Primary Sjögren's syndrome Dermato-/polymyositis Systemic sclerosis Rheumatoid arthritis Reactive arthritis Antiphospholipid syndrome
adaptiert nach Praxis 2020; 109 (5): 325–331