An enchondroma is a type of noncancerous bone tumor that begins in
Enchondromas are the most common, nonaggressive lesions of the hands. More than 50% of enchondromas occur in the diaphyses of the short, tubular bones of the hands and feet. The metaphysis is the site of origin when the long tubular bones are affected. Malignant transformation occurs in 1% of solitary enchondromas, usually arising in lesions of the long, tubular or flat bones and is not a valid concern in phalangeal enchondromas.
Enchondromatosis (Ollier’s disease) is a rare, nonhereditary disorder consisting of widespread involvement of predominantly one side of the body with multiple, asymmetrically distributed enchondromas. Often there is associated shortening and deformity of the long bones affected. Malignant transformation of an individual lesion in Ollier’s disease is common, occurring in one third to one half of patients. Maffucci’s syndrome is a rare, congenital disorder of mesodermal dysplasia characterized by enchondromatosis and soft tissue hemangiomas. Malignant transformation is common.